Deep benign fibrous histiocytoma of the retropharyngeal region - A rare case report

• Author Details:   
• Pawan Nikhra ^*
• Priyanka Sharma

Deep benign fibrous histiocytoma (DBFH) is a rare, non-cancerous soft tissue tumor that typically arises in deep dermal or sub-cutaneous tissues. It is characterized by combination of fibroblastic and histiocytic cells. DBFH predominantly affects adults, with a preference for the limbs and trunk. The tumor often presents as a slow-growing, painless mass that may remain undiagnosed for a long period of time due to its indolent nature. DBFH should be differentiated from other soft tissue tumors, including malignant variants. This case report aims to present a rare instance of DBFH in a 50-year-old female with unusual site of presentation along with providing insights into its clinical presentation, diagnostic challenges, and treatment options.
DBFH is a rare, benign tumor with a slow progression and a low recurrence rate if properly excised. It poses diagnostic challenges due to its similarity with malignant tumors. Surgical excision remains the primary treatment, and close follow-up is essential to monitor for recurrence. Although the tumor follows an indolent course, accurate diagnosis and differentiation from malignant soft tissue tumors are crucial.

Keywords: Mesenchymal, Dermatofibrosarcoma protuberans, Soft tissue, Immununohistochemistry, Benign.