Melanotic neuroectodermal tumour of infancy in maxilla of a 5-month-old infant: A case report

• Author Details:   
• Jayati Tripathi
• Vibha R Vyas ^*
• Bidyut Bikash Gogoi
• Deepa Nagarajan

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Melanotic neuroectodermal tumour of infancy (MNTI) is a rare biphasic tumour composed of small neuroblast-like cells and larger melanin-producing epithelial cells. Most tumours (>90%) occur in the craniofacial bones where maxilla is the most common site (> 60%) as was in our case, followed by skull (~15%) and mandible (~8%); soft tissue tumours are rare. Most common presentation is as a sessile, painless, rapidly enlarging mass in the upper alveolus which causes facial deformity and feeding disruption. We are presenting an interesting case of MNTI which came to our institute.

Keywords: Melanotic neuroectodermal tumour of infancy, Biphasic tumour, Maxilla.