Mixed germ cell tumors of the ovary are rare neoplasms that often occur in young females and consist of two or more histological germ cell components. We present a rare case of an ovarian mixed germ cell tumor comprising dysgerminoma, yolk sac tumor, and residual gonadoblastoma in 8 year-old phenotypic female with abdominal pain and a pelvic mass. Histopathological evaluation revealed predominant dysgerminoma, with distinct areas of yolk sac tumor and microscopic foci of residual gonadoblastoma. The case highlights the importance of thorough histological examination for accurate diagnosis and appropriate management. This paper also includes a review of the relevant literature, discussing pathogenesis, clinical presentation, diagnostic approach, treatment strategies, and prognosis.
Keywords: Endodermal sinus tumors, Gonadoblastoma, Histopathologica.