The primordial odontogenic tumor (POT) is a recently described benign entity with histopathological and immunohistochemical features suggesting its origin during early odontogenesis that has been included in the World Health Organization classification 2017. Only 27 cases that conform to the clinico-pathologic criteria for diagnosis have been reported worldwide. We report an case of POT in a 9-year-old child patient who presented with diffuse swelling in pre-auricular region. Large expansile osteoytic lesion involving inverted 47 causing erosion of superior margin with persistent expansion of buccal and lingual cortical plate was observed radiographically. Along with the present case, we also present here a summary of the cases reported till date and the review of literature.
odontogenic,Primordial,epithelial